KLRB1

killer cell lectin like receptor B1, the group of Killer cell lectin like receptors|C-type lectin domain containing|CD molecules

Basic information

Region (hg38): 12:9594551-9607916

Previous symbols: [ "NKR" ]

Links

ENSG00000111796NCBI:3820OMIM:602890HGNC:6373Uniprot:Q12918AlphaFoldGenCCjaxSfariGnomADPubmedClinVar

Phenotypes

GenCC

Source: genCC

No genCC data.

ClinVar

This is a list of variants' phenotypes submitted to ClinVar and linked to the KLRB1 gene.

  • not_specified (40 variants)
  • not_provided (2 variants)

Variants pathogenicity by type

Statistics on ClinVar variants can assist in determining whether a specific variant type in the KLRB1 gene is commonly pathogenic or not. These statistics are base on transcript: NM_000002258.3. Only rare variants are included in the table.

In the table, we include only reliable ClinVar variants with their consequences to MANE Select, Mane Plus Clinical transcripts, or transcripts with TSL equals 1. Click the count to view the source variants.

Warning: slight differences between displayed counts and the number of variants in ClinVar may occur, primarily due to (1) the application of a different transcript and/or consequence by our variant effect predictor or (2) differences in clinical significance: we classify Benign/Likely benign variants as Likely benign and Pathogenic/Likely pathogenic variants as Likely pathogenic.

EffectPLPVUSLBBSum
synonymous
0
missense
38
clinvar
2
clinvar
40
nonsense
0
start loss
0
frameshift
0
splice donor/acceptor (+/-2bp)
0
Total 0 0 38 2 0
Loading clinvar variants...

GnomAD

Source: gnomAD

GeneTypeBio TypeTranscript Coding Exons Length
KLRB1protein_codingprotein_codingENST00000229402 613336
pLI Probability
LOF Intolerant
pRec Probability
LOF Recessive
Individuals with
no LOFs
Individuals with
Homozygous LOFs
Individuals with
Heterozygous LOFs
Defined p
2.41e-70.293125716081257240.0000318
Z-Score Observed Expected Observed/Expected Mutation Rate Total Possible in Transcript
Missense0.1331061100.9640.000005211449
Missense in Polyphen1525.8360.58059392
Synonymous0.8653340.00.8260.00000189415
Loss of Function0.4171112.60.8736.85e-7140

LoF frequencies by population

EthnicitySum of pLOFs p
African & African-American0.00009300.0000929
Ashkenazi Jewish0.000.00
East Asian0.0002180.000217
Finnish0.000.00
European (Non-Finnish)0.00001760.0000176
Middle Eastern0.0002180.000217
South Asian0.000.00
Other0.000.00

dbNSFP

Source: dbNSFP

Function
FUNCTION: Plays an inhibitory role on natural killer (NK) cells cytotoxicity. Activation results in specific acid sphingomyelinase/SMPD1 stimulation with subsequent marked elevation of intracellular ceramide. Activation also leads to AKT1/PKB and RPS6KA1/RSK1 kinases stimulation as well as markedly enhanced T-cell proliferation induced by anti-CD3. Acts as a lectin that binds to the terminal carbohydrate Gal-alpha(1,3)Gal epitope as well as to the N-acetyllactosamine epitope. Binds also to CLEC2D/LLT1 as a ligand and inhibits NK cell-mediated cytotoxicity as well as interferon-gamma secretion in target cells. {ECO:0000269|PubMed:16455998, ECO:0000269|PubMed:16925668, ECO:0000269|PubMed:8077657}.;
Pathway
Malaria - Homo sapiens (human);Immune System;Immunoregulatory interactions between a Lymphoid and a non-Lymphoid cell;Adaptive Immune System (Consensus)

Intolerance Scores

loftool
0.803
rvis_EVS
0.39
rvis_percentile_EVS
76.05

Haploinsufficiency Scores

pHI
0.0854
hipred
N
hipred_score
0.112
ghis
0.413

Essentials

essential_gene_CRISPR
N
essential_gene_CRISPR2
N
essential_gene_gene_trap
N
gene_indispensability_pred
N
gene_indispensability_score
0.0670

Gene Damage Prediction

AllRecessiveDominant
MendelianMediumMediumMedium
Primary ImmunodeficiencyHighMediumHigh
CancerHighHighHigh

Mouse Genome Informatics

Gene name
Klrb1c
Phenotype

Gene ontology

Biological process
cell surface receptor signaling pathway;regulation of immune response
Cellular component
plasma membrane;integral component of membrane
Molecular function
transmembrane signaling receptor activity;protein binding;carbohydrate binding