LACTB2

protein-coding

lactamase beta 2, the group of MBL domain containing glyoxalase 2 subfamily

Gene summary

Enables RNA endonuclease activity; single-stranded RNA binding activity; and zinc ion binding activity. Located in several cellular components, including Golgi apparatus; mitochondrial matrix; and nucleoplasm. [provided by Alliance of Genome Resources, Jun 2026]

MANE transcript

NM_016027.3

Inheritance

—

ClinVar variants

U:49B:4

Top phenotype

LACTB2-related condition

gnomAD constraint

pLI —, LoF o/e 0.62

Max pathogenic AF

—

Genomic locus

chr8:70,635,318-70,669,185

External References & Databases

Transcript & Mutation Effects

hg38 • Region Span ~33.9 kb
Loading mutation effect viewer...

GenCC Phenotypes & Disease Associations

Curated gene-disease validity assertions and inheritance patterns

No GenCC data available for this gene.

ClinVar Associated Diseases & Phenotypes

Reported disease conditions connected to LACTB2 variants in ClinVar

2 Conditions Cataloged
not specifiedTotal: 46
LACTB2-related conditionTotal: 1

ClinVar Variants & Pathogenicity by Type

Statistics based on transcript NM_016027.3. Only rare variants are included.

We include only reliable ClinVar variants with their consequences to MANE Select, MANE Plus Clinical transcripts, or transcripts with TSL equal to 1. Click a count to filter the variants table below.

Slight differences between displayed counts and ClinVar may occur due to a different transcript/consequence chosen by our variant effect predictor, or because we classify Benign/Likely benign as Likely benign and Pathogenic/Likely pathogenic as Likely pathogenic.

EffectPLPVUSLBBSum
synonymous
0
missense
45
clinvar
4
clinvar
49
nonsense
0
start loss
0
frameshift
1
clinvar
1
splice donor/acceptor (+/-2bp)
3
clinvar
3
Total00494053
Loading ClinVar variants...

Transcript Catalog

Annotated transcript isoforms across RefSeq and Ensembl databases

Showing 4 of 24 transcripts
Transcript IDSourceProtein IDCoding ExonsMANE Status
NM_016027.3RefSeqNP_057111.17MANE Select
ENST00000276590.5EnsemblENSP00000276590.47MANE Select
ENST00000522447.5EnsemblENSP00000428801.17Standard
ENST00000522447.6EnsemblENSP00000428801.17Standard

Gene Ontology (GO) Annotations & Pathways

Biological processes, molecular functions, cellular components and pathways

Biological Process

  • RNA phosphodiester bond hydrolysis, endonucleolytic

Molecular Function

  • single-stranded RNA binding
  • endoribonuclease activity
  • protein binding
  • zinc ion binding

Cellular Component

  • mitochondrial matrix

gnomAD Constraint

Source: gnomAD

Gene type
protein_coding
Transcript type
protein_coding
Transcript
ENST00000276590
Coding exons
7
Length
33857
Individuals with no LoFs
125716
Homozygous LoFs
1
Heterozygous LoFs
30
Defined
125747
p
0.000123
Z-ScoreObservedExpectedObserved/ExpectedMutation RateTotal Possible
Missense0.4331301450.8990.000006761878
Missense (PolyPhen)3739.6820.93241497
Synonymous0.7294450.60.8700.00000228536
Loss of Function1.32914.40.6247.56e-7183

Population LoF Frequency

PopulationCAFp-valueStatus
African0.000310.00031rare
Latino/Admixed American0.0000870.000087rare
Ashkenazi Jewish00.0absent
East Asian0.000220.00022rare
Finnish0.0000460.000046rare
European (Non-Finnish)0.000120.00012rare
South Asian0.000160.00013rare
Other00.0absent

dbNSFP Gene Annotations

Source: dbNSFP

Function
FUNCTION: Endoribonuclease; cleaves preferentially 3' to purine- pyrimidine dinucleotide motifs in single-stranded RNA. The cleavage product contains a free 3' -OH group. Has no activity with double-stranded RNA or DNA. Required for normal mitochondrial function and cell viability. {ECO:0000269|PubMed:26826708}.;

Recessive Scores

pRec
0.0908

Intolerance Scores

LoFtool
0.655
RVIS EVS
-0.27
RVIS percentile EVS
33.97

Essentials

Essential (CRISPR)
N
Essential (CRISPR2)
N
Essential (gene trap)
N
Indispensability pred.
E
Indispensability score
0.928

Gene Damage Prediction

AllRecessiveDominant
MendelianMediumMediumMedium
Primary ImmunodeficiencyMediumMediumMedium
CancerMediumMediumMedium
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