LGR6

protein-coding

leucine rich repeat containing G protein-coupled receptor 6, the group of G protein-coupled receptors, Class A orphans

Gene summary

This gene encodes a member of the leucine-rich repeat-containing subgroup of the G protein-coupled 7-transmembrane protein superfamily. The encoded protein is a glycoprotein hormone receptor with a large N-terminal extracellular domain that contains leucine-rich repeats important for the formation of a horseshoe-shaped interaction motif for ligand binding. Alternative splicing of this gene results in multiple transcript variants. [provided by RefSeq, Jul 2008]

MANE transcript

NM_001017403.2

Inheritance

—

ClinVar variants

U:146B:14

Top phenotype

—

gnomAD constraint

pLI —, LoF o/e 0.42

Max pathogenic AF

—

Genomic locus

chr1:202,193,799-202,319,781

External References & Databases

Transcript & Mutation Effects

hg38 • Region Span ~126.0 kb
Loading mutation effect viewer...

GenCC Phenotypes & Disease Associations

Curated gene-disease validity assertions and inheritance patterns

No GenCC data available for this gene.

ClinVar Associated Diseases & Phenotypes

Reported disease conditions connected to LGR6 variants in ClinVar

2 Conditions Cataloged
not specifiedTotal: 146
not providedTotal: 8

ClinVar Variants & Pathogenicity by Type

Statistics based on transcript NM_001017403.2. Only rare variants are included.

We include only reliable ClinVar variants with their consequences to MANE Select, MANE Plus Clinical transcripts, or transcripts with TSL equal to 1. Click a count to filter the variants table below.

Slight differences between displayed counts and ClinVar may occur due to a different transcript/consequence chosen by our variant effect predictor, or because we classify Benign/Likely benign as Likely benign and Pathogenic/Likely pathogenic as Likely pathogenic.

EffectPLPVUSLBBSum
synonymous
3
clinvar
5
clinvar
2
clinvar
10
missense
140
clinvar
6
clinvar
1
clinvar
147
nonsense
0
start loss
0
frameshift
0
splice donor/acceptor (+/-2bp)
3
clinvar
3
Total00146113160
Loading ClinVar variants...

Transcript Catalog

Annotated transcript isoforms across RefSeq and Ensembl databases

Showing 4 of 82 transcripts
Transcript IDSourceProtein IDCoding ExonsMANE Status
NM_001017403.2RefSeqNP_001017403.118MANE Select
ENST00000367278.8EnsemblENSP00000356247.318MANE Select
NM_001017404.2RefSeqNP_001017404.116Standard
NM_021636.3RefSeqNP_067649.218Standard

Gene Ontology (GO) Annotations & Pathways

Biological processes, molecular functions, cellular components and pathways

Pathways ConsensusPathDB

  • GPCRs, Other
  • Signaling by WNT
  • Signal Transduction
  • Regulation of FZD by ubiquitination
  • TCF dependent signaling in response to WNT

Biological Process

  • G protein-coupled receptor signaling pathway
  • Wnt signaling pathway
  • positive regulation of Wnt signaling pathway
  • positive regulation of cell migration
  • positive regulation of canonical Wnt signaling pathway

Molecular Function

  • transmembrane signaling receptor activity
  • G protein-coupled receptor activity
  • protein binding
  • protein-hormone receptor activity

Cellular Component

  • plasma membrane
  • integral component of plasma membrane
  • vesicle
  • trans-Golgi network membrane

gnomAD Constraint

Source: gnomAD

Gene type
protein_coding
Transcript type
protein_coding
Transcript
ENST00000367278
Coding exons
18
Length
125881
Individuals with no LoFs
125708
Homozygous LoFs
0
Heterozygous LoFs
40
Defined
125748
p
0.000159
Z-ScoreObservedExpectedObserved/ExpectedMutation RateTotal Possible
Missense1.074825530.8720.00003206143
Missense (PolyPhen)170223.760.759752606
Synonymous0.4962452550.9600.00001552105
Loss of Function3.311638.00.4210.00000177431

Population LoF Frequency

PopulationCAFp-valueStatus
African0.0000620.000062rare
Latino/Admixed American0.0000870.000087rare
Ashkenazi Jewish0.000220.00020rare
East Asian0.000110.00011rare
Finnish00.0absent
European (Non-Finnish)0.000150.00015rare
South Asian0.000430.00042rare
Other0.000330.00033rare

dbNSFP Gene Annotations

Source: dbNSFP

Function
FUNCTION: Receptor for R-spondins that potentiates the canonical Wnt signaling pathway and acts as a marker of multipotent stem cells in the epidermis. Upon binding to R-spondins (RSPO1, RSPO2, RSPO3 or RSPO4), associates with phosphorylated LRP6 and frizzled receptors that are activated by extracellular Wnt receptors, triggering the canonical Wnt signaling pathway to increase expression of target genes. In contrast to classical G-protein coupled receptors, does not activate heterotrimeric G-proteins to transduce the signal. May act as a tumor suppressor. {ECO:0000269|PubMed:21727895, ECO:0000269|PubMed:22615920}.;

Intolerance Scores

LoFtool
0.232
RVIS EVS
-0.1
RVIS percentile EVS
45.69

Essentials

Essential (CRISPR)
N
Essential (CRISPR2)
N
Essential (gene trap)
N
Indispensability pred.
N
Indispensability score
0.0700

Gene Damage Prediction

AllRecessiveDominant
MendelianMediumMediumMedium
Primary ImmunodeficiencyMediumMediumMedium
CancerMediumMediumMedium
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