SEC31B

protein-coding

SEC31 homolog B, COPII coat complex component, the group of COPII coat complex|WD repeat domain containing

Gene summary

This gene encodes a protein of unknown function. The protein has moderate similarity to rat VAP1 protein which is an endosomal membrane-associated protein, containing a putative Ca2+/calmodulin-dependent kinase II phosphorylation site. [provided by RefSeq, Jul 2008]

Previous symbols:
  • SEC31L2

MANE transcript

NM_015490.4

Inheritance

—

ClinVar variants

U:184B:17

Top phenotype

—

gnomAD constraint

pLI —, LoF o/e 0.83

Max pathogenic AF

—

Genomic locus

chr10:100,486,646-100,519,864

External References & Databases

Transcript & Mutation Effects

hg38 • Region Span ~33.2 kb
Loading mutation effect viewer...

GenCC Phenotypes & Disease Associations

Curated gene-disease validity assertions and inheritance patterns

No GenCC data available for this gene.

ClinVar Associated Diseases & Phenotypes

Reported disease conditions connected to SEC31B variants in ClinVar

2 Conditions Cataloged
not specifiedTotal: 191
not providedTotal: 2

ClinVar Variants & Pathogenicity by Type

Statistics based on transcript NM_015490.4. Only rare variants are included.

We include only reliable ClinVar variants with their consequences to MANE Select, MANE Plus Clinical transcripts, or transcripts with TSL equal to 1. Click a count to filter the variants table below.

Slight differences between displayed counts and ClinVar may occur due to a different transcript/consequence chosen by our variant effect predictor, or because we classify Benign/Likely benign as Likely benign and Pathogenic/Likely pathogenic as Likely pathogenic.

EffectPLPVUSLBBSum
synonymous
3
clinvar
1
clinvar
4
missense
180
clinvar
16
clinvar
196
nonsense
1
clinvar
1
start loss
0
frameshift
0
splice donor/acceptor (+/-2bp)
0
Total00184170201
Loading ClinVar variants...

Transcript Catalog

Annotated transcript isoforms across RefSeq and Ensembl databases

Showing 4 of 26 transcripts
Transcript IDSourceProtein IDCoding ExonsMANE Status
NM_015490.4RefSeqNP_056305.125MANE Select
ENST00000370345.8EnsemblENSP00000359370.325MANE Select
ENST00000462434.5EnsemblENSP00000474124.18Standard
ENST00000469546.6EnsemblENSP00000435359.18Standard

Model Organisms & Knockout Phenotypes

Observed phenotypic effects in mouse and zebrafish models

Gene / ModelOrganismObserved Phenotype
sec31bDanio rerio

Structure: intestine

Quality: decreased size

abnormal

Gene Ontology (GO) Annotations & Pathways

Biological processes, molecular functions, cellular components and pathways

Pathways ConsensusPathDB

  • Protein processing in endoplasmic reticulum - Homo sapiens (human)
  • Sterol Regulatory Element-Binding Proteins (SREBP) signalling

Biological Process

  • intracellular protein transport
  • endoplasmic reticulum to Golgi vesicle-mediated transport
  • endoplasmic reticulum organization
  • COPII-coated vesicle cargo loading
  • COPII-coated vesicle budding

Molecular Function

  • structural molecule activity

Cellular Component

  • Golgi membrane
  • endoplasmic reticulum membrane
  • vesicle coat
  • COPII vesicle coat
  • endoplasmic reticulum exit site

gnomAD Constraint

Source: gnomAD

Gene type
protein_coding
Transcript type
protein_coding
Transcript
ENST00000370345
Coding exons
25
Length
43230
Individuals with no LoFs
125392
Homozygous LoFs
1
Heterozygous LoFs
355
Defined
125748
p
0.00142
Z-ScoreObservedExpectedObserved/ExpectedMutation RateTotal Possible
Missense0.06196186220.9930.00003147589
Missense (PolyPhen)105112.890.930141521
Synonymous-0.07852492471.010.00001242434
Loss of Function1.225060.30.8300.00000289685

Population LoF Frequency

PopulationCAFp-valueStatus
African0.00360.0036notable
Latino/Admixed American0.00210.0021notable
Ashkenazi Jewish00.0absent
East Asian0.00370.0037notable
Finnish0.0000470.000046rare
European (Non-Finnish)0.00110.0011notable
South Asian0.000950.00095rare
Other0.000810.00065rare

dbNSFP Gene Annotations

Source: dbNSFP

Function
FUNCTION: As a component of the coat protein complex II (COPII), may function in vesicle budding and cargo export from the endoplasmic reticulum. {ECO:0000269|PubMed:16495487}.;

Recessive Scores

pRec
0.0776

Intolerance Scores

LoFtool
0.974
RVIS EVS
2.08
RVIS percentile EVS
97.82

Essentials

Essential (CRISPR)
N
Essential (CRISPR2)
N
Essential (gene trap)
N
Indispensability pred.
N
Indispensability score
0.0500

Gene Damage Prediction

AllRecessiveDominant
MendelianHighHighHigh
Primary ImmunodeficiencyHighHighHigh
CancerHighHighHigh
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