TRIM26

protein-coding

tripartite motif containing 26, the group of Tripartite motif family|Ring finger proteins

Gene summary

The protein encoded by this gene is a member of the tripartite motif (TRIM) family. The TRIM motif includes three zinc-binding domains, a RING, a B-box type 1 and a B-box type 2, and a coiled-coil region. The protein localizes to cytoplasmic bodies. Although the function of the protein is unknown, the RING domain suggests that the protein may have DNA-binding activity. The gene localizes to the major histocompatibility complex (MHC) class I region on chromosome 6. Alternatively spliced transcript variants encoding the same protein have been found for this gene. [provided by RefSeq, Jun 2011]

Previous symbols:
  • ZNF173

MANE transcript

NM_003449.5

Inheritance

—

ClinVar variants

U:54B:14

Top phenotype

—

gnomAD constraint

pLI —, LoF o/e 0.25

Max pathogenic AF

—

Genomic locus

chr6:30,184,455-30,213,427

External References & Databases

Transcript & Mutation Effects

hg38 • Region Span ~29.0 kb
Loading mutation effect viewer...

GenCC Phenotypes & Disease Associations

Curated gene-disease validity assertions and inheritance patterns

No GenCC data available for this gene.

ClinVar Associated Diseases & Phenotypes

Reported disease conditions connected to TRIM26 variants in ClinVar

1 Conditions Cataloged
not specifiedTotal: 61

ClinVar Variants & Pathogenicity by Type

Statistics based on transcript NM_003449.5. Only rare variants are included.

We include only reliable ClinVar variants with their consequences to MANE Select, MANE Plus Clinical transcripts, or transcripts with TSL equal to 1. Click a count to filter the variants table below.

Slight differences between displayed counts and ClinVar may occur due to a different transcript/consequence chosen by our variant effect predictor, or because we classify Benign/Likely benign as Likely benign and Pathogenic/Likely pathogenic as Likely pathogenic.

EffectPLPVUSLBBSum
synonymous
0
missense
49
clinvar
14
clinvar
63
nonsense
0
start loss
0
frameshift
0
splice donor/acceptor (+/-2bp)
5
clinvar
5
Total005414068
Loading ClinVar variants...

Transcript Catalog

Annotated transcript isoforms across RefSeq and Ensembl databases

Showing 4 of 94 transcripts
Transcript IDSourceProtein IDCoding ExonsMANE Status
NM_003449.5RefSeqNP_003440.17MANE Select
ENST00000454678.7EnsemblENSP00000410446.27MANE Select
NM_001242783.2RefSeqNP_001229712.17Standard
ENST00000416596.5EnsemblENSP00000413673.13Standard

Gene Ontology (GO) Annotations & Pathways

Biological processes, molecular functions, cellular components and pathways

Pathways ConsensusPathDB

  • Cytokine Signaling in Immune system
  • Immune System
  • Interferon gamma signaling
  • Interferon Signaling

Biological Process

  • innate immune response
  • negative regulation of viral entry into host cell
  • positive regulation of DNA-binding transcription factor activity
  • interferon-gamma-mediated signaling pathway
  • negative regulation of viral release from host cell

Molecular Function

  • DNA binding
  • protein binding
  • zinc ion binding
  • transferase activity
  • metal ion binding

Cellular Component

  • cellular_component
  • nucleus
  • cytosol

gnomAD Constraint

Source: gnomAD

Gene type
protein_coding
Transcript type
protein_coding
Transcript
ENST00000454678
Coding exons
7
Length
28973
Individuals with no LoFs
123418
Homozygous LoFs
0
Heterozygous LoFs
15
Defined
123433
p
0.0000608
Z-ScoreObservedExpectedObserved/ExpectedMutation RateTotal Possible
Missense3.091713290.5200.00002093464
Missense (PolyPhen)3087.7850.341741027
Synonymous0.9521271410.8980.000009081057
Loss of Function3.71728.30.2470.00000163299

Population LoF Frequency

PopulationCAFp-valueStatus
African00.0absent
Latino/Admixed American00.0absent
Ashkenazi Jewish0.000100.00010rare
East Asian0.0000550.000055rare
Finnish00.0absent
European (Non-Finnish)0.000110.00011rare
South Asian00.0absent
Other0.000170.00016rare

dbNSFP Gene Annotations

Source: dbNSFP

Function
FUNCTION: E3 ubiquitin-protein ligase which regulates the IFN-beta production and antiviral response downstream of various DNA- encoded pattern-recognition receptors (PRRs). Promotes nuclear IRF3 ubiquitination and proteasomal degradation. Bridges together TBK1 and NEMO during the innate response to viral infection leading to the activation of TBK1. {ECO:0000269|PubMed:25763818, ECO:0000269|PubMed:26611359}.;

Intolerance Scores

LoFtool
0.437
RVIS EVS
-0.56
RVIS percentile EVS
19.73

Essentials

Essential (CRISPR)
N
Essential (CRISPR2)
N
Essential (gene trap)
N
Indispensability pred.
E
Indispensability score
0.987

Gene Damage Prediction

AllRecessiveDominant
MendelianMediumMediumMedium
Primary ImmunodeficiencyMediumMediumMedium
CancerMediumMediumMedium
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